1) Cat. No.: TRC-M335000; 2) Chemical Name: 4-Methylumbelliferyl 6-Sulfo-2-acetamido-2-deoxy-β-D-glucopyranoside Potassium Salt ; 3) CAS No.: 210357-38-3; 4) Mol. Formula: C18H20KNO11S; 5) Mol. Weight: 497.51; 6) Packing Size: 100mg / 1g; 7) Appearence: White Solid; 8) Application Notes: A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis.  They include Tay Sachs disease, Sandhoff disease and other forms.; 9) Synonym: 7-[[2-(Acetylamino)-2-deoxy-6-O-sulfo-β-D-glucopyranosyl]oxy]-4-methyl-2H-1-benzopyran-2-one